Shishir Ram SHETTY, Anusha RANGARE, Priya Sara THOMAS, Subhas Babu G

Mandibüler ve Palatal Anormallikle Beraber Sendromik Olmayan Hipoglossi

Dil; konuşma, çiğneme , tatma ve yutma gibi birçok fonksiyona sahip, vücudumuzun en hareketli organıdır. Literatürde dilin sayısız konjenital ve kalıtımsal bozuklukları bildirilmiştir. Mikroglossi olarak da bilinen hipoglossi nadir anomalilerden biridir. Çoğunlukla diğer sistemik anormalliklerle ilişkilidir ancak nadiren izole bir antite olarak bulunur. Dilin gelişmesindeki yokluk düşük mandibüler gelişmeye yol açar. Bu yazının amacı nadir bir izole hipoglossi ve sebep olduğu mikrognatiyi sunmaktır. Hastamızda çok çok nadir görülen hipoglossiye eşlik eden palatal ve faucial pillar anormallikler de vurgulanmıştır.

Anahtar Kelimeler:

Hipoglossi, mikrognati, palatal anormallikler

Non Syndromic Hypoglossia With Mandibular and Palatal Abnormalities

Tongue is the most mobile organ of the body with multiple functions such as speech, mastication, taste and swallowing. Numerous congenital and developmental disorders of the tongue have been reported in literature. Hypoglossia also known as microglossia is one of the rare anomalies. Usually hypoglossia is associated with many other systemic abnormalities but rarely found as an isolated entity. Lack of tongue development leads to decreased mandibular growth. The aim of this article is to report a rare case of isolated hypoglossia and resultant micrognathia. Presence of palatal and faucial pillar abnormalities with hypoglossia which is extremely rare is also highlighted in our report.

Keywords:

Hypoglossia, micrognathia, palatal abnormalities.,

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