Shruthi HEGDE, Vidya UPADHYAYA, Praveen BN, Shubhasini AR, Subhas BABU, Shishir Ram SHETTY, Vidya AJİLA

Lenfanjiomatozisin Tanısal Görüntülemesi – Resimlerle Genel Bakış

Lenfanjiomatozis; kemikler, parankimal organlar ve yumuşak dokuyu kapsayan lenf kanallarının diffüz proliferasyonu ile karakterize nadir görülen konjenital bir bozukluktur. Lenfanjiomatozis sıklıkla geç çocuklukta görülür. Birden çok kemiklerde litik lezyonlar oluşturur. Hastalığın prognozu iyi huylu durumdan ölümcül hale kadar çeşitli şekillerde rapor edilmiştir. Biz özellikle mandibula tutulumu olan lenfanjiomatozisli 14 yaşındaki bir kız klinik ve görüntüleme bulguları sunuldu.

Anahtar Kelimeler:

lenfanjiomatozis, mandibula, lenfanjiyom

Diagnostic Imaging of Lymphangiomatosis- A Pictorial Overview

Lymphangiomatosis is a rare congenital disorder, characterized by a diffuse proliferation of lymphatic channels involving bones, parenchymal organs, and soft tissue. Lymphangiomatosis frequently presents in late childhood. It produces lytic lesions in multiple bones. Prognosis of the disease has been variously reported from benign to fatal. We present the clinical and imaging features of a 14-year old girl with lymphangiomatosis and particularly involvement of mandible.

Keywords:

Lymphangiomatosis, mandible, lymphangioma,

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Nishimura M, Segami N, Kaneyama K, Sato J. Systemic lymphangiomatosis of bone involving the mandible with cystic hygroma of the neck. J Oral Maxillofac Surg. 2006 Jul;64(7):115760.
Yang DH, Goo HW. Generalized Lymphangiomatosis: Radiologic Findings in Three Pediatric Patients. Korean J Radiol 2006;7:287-291
Méndez JA , Hochmuth A, Boetefuer IC , Schumacher M. Radiologic Appearance of a Rare Primary Vertebral Lymphangioma. AJNR Am J Neuroradiol 2002;23: 1665-1668.
GC Gan, ML Wastie. Lymphangiomatosis: a wide spectrum of disease. J Hong Kong Col Radiol 2010;13:222-5.
Nagar AM, Bhatgadde VL, Raut AA, Narlawar RS. Skeletal lymphangiomatosis with chylous pleural effusion. The Journal of Radiology 2003 Faul J, Berry G, Colby T, et al. Thoracic lymphangiomas, lymphangiectasis, lymphangiomatosis, and lymphatic dysplasia syndrome. Am J Respir Crit Care Med 2000;161:1037–1046.
Kupeli S , Arac A,Yalc B¸ Sokmensuer C, Buyukpamukcu M. Lymphangiomatosis in a child: Eight Years’ Follow-Up Without Treatment. Pediatric Hematology and Oncology, 2008, 25:614– 619.
Brown RR, Pathria MN, Ruggieri PM, Jacobson JA, Craig JG, Resnick D. Extensive intraosseous gas associated with lymphangiomatosis of bone: report of three cases. Radiology 1997;205:260-262.
Marom EM, Moran CA, Munden RF. Generalized Lymphangiomatosis. AJR 2004;182:1068.
Nishimura M, Segami N, Kaneyama K, Sato J. Systemic lymphangiomatosis of bone involving the mandible with cystic hygroma of the neck. J Oral Maxillofac Surg. 2006 Jul;64(7):115760.