Artrogripozis Multipleks Konjenita ve Anestezi: Olgu Sunumu ve Literatürün Gözden Geçirilmesi
Artrogripozis multipleks konjenita nadir görülen bir konjenital sendromu tanımlayan terimdir. Klinik tablo, tekrarlayan cerrahi girişimler gerektiren multipl eklem kontraktürleriyle karakterizedir. Çeşitli sistem anomalileri bu sendroma eşlik edebilir. Artrogripozis multipleks konjenitalı hastada anestezi yönetimi; zor havayolu, zor damaryolu ve malign hipertermiyi içeren birçok zorluğa yol açabilir. Biz bu olgu sunumunda, eklem kontraktürü için opere edilen 13 aylık erkek çocuğunun anestezi yönetimini tartışmayı amaçladık.
Arthrogrypozis Multiplex Congenita and Anesthesia: A Case Report and Review of the Literature
Arthrogryposis Multiplex Congenita is a term that describes a rare congenital syndrome. Clinical features is characterized by multiple joint contractures that requires recurrent surgical interventions. Various system anomalies can be associated with this syndrome. The anesthesia management of a patient with Arthrogryposis Multiplex Congenita may lead to several challenges including difficult airway, difficult venous access and malign hyperthermia. In this case report, we aimed to present the anesthesia management of a 13 months-old case with arthrogryposis multiplex congenita who operated for joint contracture.
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