Önder YAVAŞCAN, Nejat AKSU, Aytaç GÜLCÜ, Meral BAYRAM TORUN, Alper SOYLU, Salih KAVUKÇU

Hypertension and multiple arterial changes in a child with Klippel Trenaunay syndrome

Klippel-Trenaunay sendromu (KTS) özellikle venöz sistemi etkileyen kalıtsal bir hastalıktır. Venöz patolojilere eşlik eden arteriyel malformasyonlar oldukça nadirdir. Biz burada hipertansiyon ve renal atrofi nedeni ile başvuran, multipl arteriyel (renal, pulmoner ve internal karotid) patolojik özelliklere sahip KTS'lu 10 yaşında bir erkek hastayı sunduk.

Klippel-Trenaunay sendromlu bir çocukta hipertansiyon ve multipl arteriyel değişiklikler

Klippel-Trenaunay syndrome (KTS) is an inherited disorder which essentially affects the venous system. Arterial malformations accompanying venous pathologies are extremely rare. We report a 10-year-old boy of KTS patient presented with hypertension and renal atrophy who have also multiple arterial (renal, pulmonary and internal carotid) pathologic features.

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