Muhammed ŞAHİN, Adnan YILDIRIM, Fatih Mehmet TÜRKCÜ, Harun YÜKSEL, Alparslan ŞAHİN

Bietti’ Crystalline Retinal Dystrophy: A Case Report

Bietti’ crystalline retinal dystrophy (BCD) is a rare, autosomal, recessively inherited disorder, characterized by the deposition of yellow crystals in the corneal limbus and retina. In this paper we aimed to present a pediatric case with BCD, with clinical, electrophysiological and spectral domain optical coherence tomography (SD-OCT) findings and discuss BCD with the light of the literature. J Clin Exp Invest 2016; 7 (1): 94-97

Keywords:

Bietti’ crystalline dystrophy, cornea, crystalline deposits, retina,

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