Kutis Marmorata Telenjiektatika Konjenita: Bir Olgu Sunumu
Kutis marmorata telenjiektatika konjenita KMTK , etyolojisi bilinmeyen, sporadik, nadir görülen, kendiliğinden solma eğiliminde olan, ısı ve hemodinami ile ilişkisiz kutis marmorata, telenjiektaziler ve flebiektazilerle karakterize kutanöz vasküler bir hastalıktır. Bazı vakalarda doğumda görülürken, sonradan da ortaya çıkabilir. Tanı klinik bulgularla konulur.Burada sol bacak ve ayakta, kalçada ve sol karın bölgesinde KMTK lezyonu olan bir kız yenidoğan olgusu sunuldu.
Anahtar Kelimeler:
Kutis marmorata telenjiektatika, yenidoğan
Cutis Marmorata Telangiectatica Congenita: A Case Report
Cutis marmorata telangiectatica congenita CMTC is an uncommon, sporadic, congenital cutanous vascular anomaly characterized by persistent cutis marmorata, telengiectasia and phlebectasia. It is generally present at birth or shortly thereafter. Physical examination helps in diagnosing CMTC.Here, we report a full-term newborn female baby with CMTC at birth with reticulated bluish purple skin changes over the skin of both left leg and foot, hip and left abdomen.
Keywords:
Cutis marmorata telangiectatica, newborn,
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- Yayın Aralığı: Yılda 4 Sayı
- Başlangıç: 2004
- Yayıncı: -
Sayıdaki Diğer Makaleler
Kutis Marmorata Telenjiektatika Konjenita: Bir Olgu Sunumu
İsmet KAHRAMAN, Nurdan URAS, Evrim ALYAMAÇ DİZDAR, Tijen ŞAHİN, Zuhal ÖZEN TUNAY