İDİYOPATİK MEDİASTİNAL FİBROZİS OLGUSU

İdiyopatik mediastinal fibrozis (İMF) mediastenin visseral kompartmanında yoğun fibröz doku proliferasyonu ve depolanmasıyla sonuçlanan, nedeni her zaman ortaya konamayan, nadir izlenen bir patolojidir. Bu makalede, daha önce bilateral akciğer kist hidatiği nedeniyle opere edilmiş, sırt ağrısı yakınmasıyla başvuran 37 yaşındaki erkek hastada, eksploratris torakotomi ve inkomplet rezeksiyonla tanısı konan bir İMF olgusu sunulmuştur.
Anahtar Kelimeler:

İdiyopatik, mediasten, fibrozis

A CASE OF IDIOPATHIC MEDIASTINAL FIBROSIS

Idiopathic mediastinal fibrosis (IMF) is a rare pathological entity characterized with a dense fibrous tissue proliferation and storage in the visseral compartment of the mediastinum. Its etiology is undetermined in most of the cases. In this report, a 37 year-old man who was previously operated for bilateral lung hidatid cysts was admitted to our department suffering from back pain. Surgical intervention revealed IMF and he was treated by incomplet resection.

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