Recep HAS, Süleyman Engin AKHAN, Sinan BERKMAN, Altay KARTAL, Ahmet Cem İYİBOZKURT, Samet TOPUZ, İbrahim KALELİOĞLU

Trap sekansı: Olgu sunumu

TRAP sekansı monokoryonik ikiz gebeliklerde 1/100 oranında görülen kötü prognoza sahip bir fenomendir. TRAP sekansında multipl anomalilere sahip, kalbi gelişmemiş “nonviable” bir fetus ile bu fetusu plasentadaki vasküler anastomozlar yoluyla besleyen pompa fetusun varlığı söz konusudur. Pompa ikiz anatomik olarak normal iken, hipoksik kan ile beslenen akardiyak ikizde gelişim vücudun alt yarısı ile sınırlıdır. Akardiyak ikiz için mortalite %100'dür. Pompa ikizin mortalitesi %50 civarında olup ölüm genellikle kalp yetmezliğine bazen de polihidramniosun yol açtığı prematüriteye bağlı olabilir. Burada antenatal dönemde tanısı koyduğumuz ve ailenin isteği doğrultusunda sonlandırılan 21 haftalık TRAP sekansı olgusu sunulmaktadır.

Trap sequence: Case report

TRAP sequence is a syndrome, seen in monochorionic twin pregnancies with poor prognosis and with a 1/100 incidence. It is characterized with a recipient fetus exhibiting lethal anomalies including acardia and a pump fetus supplying blood by vascular communications in the placenta. While pump twin is anatomically normal, in recipient twin who is supplied with hypoxic blood, the development is restricted with the lower part of the body. Mortality of acardiac twin is inevitable. Pump twin has the mortality rate of 50% and death is usually due to heart failure or premature labor caused by polihydramnios. Here, a TRAP sequence case with 21 weeks' of gestation diagnosed in antenatal period and terminated with the demand of the family is presented. Clinical presentation and therapeutic options were discussed in this case report.

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