Sema UGURALP, Unsal OZGEN, Kubulay GURUNLUOGLU, Nusret AKPOLAT, Ahmet SİGİRCİ

Clear cell sarcoma of the kidney in a newborn

Bu makalede, 37 haftalık, gebelik süresince herhangi bir sağlık kurumunda tıbbi takibi olmadan normal vajinal yolla doğan, doğumun ardından yenidoğan ünitesinde karnında kitle fark edilen bir erkek yenidoğan olgu sunuldu. Cerrahi olarak çıkarılan kitlenin histo-patolojik incelemesinde kitlenin böbrek kaynaklı clear cell sarkoması olduğu tesbit edildi. Olgudaki mevcut bulgular sunulup, böbreğin clear cell sarkomasının çocukluk çağı ve yenidoğan döneminde ortaya çıkışı ile ilgili literatür araştırması yapılarak bununla ilgili vakalar bildirildi. Yenidoğan döneminde böbreğin clear cell sarkomasının klinik olarak ortaya çıkış şekilleri, evresi, yönetimi ve sonuçları anlatıldı. Böbreğin clear cell sarkomasının yenidoğan döneminde oldukça nadir görülmesine rağmen ayrıcı tanıda akılda tutulması gerektiği vurgulandı.

Bir yenidoğanda böbreğin clear cell sarkoması

In the present article, we present the case of a 37-month-old male newborn, who was delivered by normal birth with no history of routine examinations during pregnancy, with an abdominal mass observed after the birth, and was eventually diagnosed with clear cell sarcoma of the kidney in the histopathology examination after the mass was dissected by surgery. We report the observed symptoms as well as related cases found in the literature related to childhood and newborn age clear cell sarcoma of the kidney. We also put forward clinical observance, stages, management and outcomes of clear cell sarcoma of the kidney during newborn. Our study underlines that clear cell sarcoma should be kept in mind during differential diagnosis although it is rarely observed in newborns.

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