Bayram KAHRAMAN, Hakkı Muammer KARAKAŞ, Ahmet Kemal FIRAT, Ayşegül SAĞIR

Lomber lateral dev meningoselli olguda direkt röntgenogram, US ve MRG bulguları

Amaç: Lomber lateral dev meningoselli olgunun görüntüleme bulgularının sunulması. Gereç ve Yöntem: Belinde şişlik nedeniyle beyin cerrahi polikliniğine baş vuran 1 yaşındaki erkek olguya meningosel ön tanısıyla ultrasonografi, alt abdomen BT tetkiki ve manyetik rezonans görüntüleme uygulandı. Sonuç: Tüm görüntüleme bulguları bir arada değerlendirildiğinde en büyüğü L4- 5 düzeyinde sol nöral foramen aracılığı ile cilt altı yağlı doku içerisine uzanan T2 A hiperintens, T1 A hipointens düzgün konturlu içerisinde nöral elemanlara ait lineer sinyal intensitelerinin izlendiği 10 x 8 x 10 cm boyutlarında, çok sayıda iki taraflı lomber lateral meningosel kesesi saptandı. Tartışma: Lateral myelomeningosel anomalisi çok nadir izlenen bir hastalık olup genetik geçişli lateral meningosel sendromu ile ilişkili olabilir. Bu nedenle lomber myelomeningosel olgusunun ultrasonografi, direkt röntgenogram, BT ve MRG bulgularını sunduk. Bu hastalığın radyolojik bulgularının bilinmesinin tanı ve tedavinin doğru yönlendirilmesinde etkili olacağını düşünüyoruz.

Giant lumbar lateral meningocele: X-ray, CT and MRI findings

Purpose:To present the imaging findings of an infrequent disease: giant lumbar lateral meningocele. Material and Methods: One year old baby who was presented to the neurosurgery outpatient clinic with a complaint of a mass on the lumbar area, underwent ultrasonography, abdominal CT and lumbar MRI. Results: The evaluation of all imaging findings revealed multiple bilateral lumbar lateral meningocele. The largest one was measured about 10 x 8 x 10 cm, enlarged the left neural foremen at the level of L4-5, extended to the subcutaneous fat and involved neural tissue. They were hypointense on T1 and hyperintense on T2 weighted images. Conclusion: Lateral myelomeningocele anomaly was seen infrequently and may be associated with a genetically inherited disease: lateral meningocele syndrome. For didactic purposes; ultrasonography, CT and MR imaging findings of a lumbar lateral myelomeningocele case were presented. To be aware of imaging and clinical findings of this rare disease will aid in the diagnosis and treatment of this anomaly.

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