Nuriye Tarakçı, Murat Konak, Munise Daye, Hüseyin Altunhan, Rahmi Örs

KUTANÖZ MASTOSİTOZ TANISI ALMIŞ YENİDOĞAN BEBEKTE ANAFLAKSİ: OLGU SUNUMU VE LİTERATÜR TARAMA

Mastositoz deri ve/veya iç organlarda aşırı mast hücre birikimi ile karakterize kutanöz ve sistemik olarak sınıflandırılan bir grup hastalıktır. Semptomlar mast hücre mediatörlerinin aşırı salınımına ve onların lokal veya sistemik etkilerine bağlıdır. Mastositozisli hastalarda semptomlar hafif olabileceği gibi hayatı tehdit eden anaflaktik reaksiyonlara da neden olabilmektedir. Anaflaktik krizler literatürde genellikle sistemik tutulum varlığında ve erişkin ya da çocukluk dönemlerinde bildirilmiştir. Biz burada bir günlük iken kutanöz mastositoz tanısı almış ve yenidoğan döneminde anaflaksi gelişen bir hastayı literatür eşliğinde sunduk.Mastocytosis is carachterized by excessive mast cell accumulation in the skin and/or internal organs. Mastocytosis is divided into two groups; systemic and cutaneous. Symptoms depend on excessive cytokine release and their local and systemic affects. Symptoms may be mild or cause life-threatening anaphylactic reactions. In the literature anaphylactic reactions reported in systemic disease of adult and childhood mastocytosis. We here present an anaphylaxis in the newborn with a diagnosis of cutaneous mastocytosis.

Anahtar Kelimeler:

kutanöz mastositoz, yenidoğan, anaflaksi

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