Ali Sami KIVRAK, Alaaddin NAYMAN, Yahya PAKSOY, Kürşat AYDIN

Van Der Knaap Hastalığı: Manyetik Rezonans Görüntüleme Bulguları

Van der Knaap hastalığı, megalensefalik lökoensefalopati ve subkortikal kistlerle karakterize nadir bir antitedir. Bu yazıda Van der Knaap hastalığı’nın radyolojik ve klinik tanı kriterlerine sahip üç pediatrik olgunun beyin manyetik rezonans görüntüleme MRG ve manyetik rezonans spektroskopi MRS bulguları sunulmuştur

Anahtar Kelimeler:

lökoensefalopati, manyetik razonans görüntüleme, manyetik rezonans spektroskopi, Van der Knaap hastalığı

Van der Knaap disease, characterized by megalencephalic leukoencephalopathy and subcortical cysts, is a rare condition. We present, in this study, cerebral magnetic resonance imaging MRI and MR spectroscopy MRS findings of three pediatric patients with radiological and clinical diagnostic criteria of this disease

Keywords:

leukoencephalopathy, magnetic resonance imaging, magnetic resonance spectroscopy, Van der Knaap disease,

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ISSN: 2602-3741
Yayın Aralığı: Yılda 6 Sayı
Başlangıç: 1997
Yayıncı: SELÇUK ÜNİVERSİTESİ > TIP FAKÜLTESİ

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