Giant pulmonary artery aneurysm associated with mild congenital pulmonary stenosis

Pulmoner arter anevrizması oldukça nadir görülen bir durumdur. Konjenital valvüler pulmoner darlıkta poststenotik pulmoner arter dilatasyon ve anevrizması gelişebilir. Sırt ağrısı şikâyeti ile gittikleri doktor tarafından kalpte üfürüm olması nedeni ile kliniğimize başvuran; pulmoner balon valvüloplasti uyguladığımız, hafif konjenital pulmoner darlık ve ana pulmoner arterde anevrizmatik genişleme ( pulmoner arter çapı; 5.6cm) saptadığımız 11 yaşındaki olguyu sunduk. Doğumsal valvüler pulmoner darlığa seconder poststenotik anevrizmal dilatasyon nadir bir klinik tablodur. Pulmoner hipertansiyon ve soldan-sağa şantlı konjenital kalp hastalığı yoksa balon valvuloplasti güvenli ve etkili bir yöntemdir.

Hafif konjenital pulmoner darlık ile ilişkili dev pulmoner arter anevrizması

Pulmonary artery aneurysm is a rare condition. Poststenotic pulmonary artery dilatation and aneurysm may occur in congenital valvular pulmonary stenosis. We present an 11-year old girl referred to our clinic due to cardiac murmur detected by a physician during evaluation for back pain. We have noted mild congenital pulmonary stenosis and aneurysmatic dilatation of the main pulmonary artery (pulmonary artery diameter 5.6 cm) and performed pulmonary balloon valvuloplasty. Poststenotic aneurysmal dilatation secondary to congenital valvular pulmonary stenosis is a rare clinical entity. Balloon valvuloplasty is a safe and effective treatment method if there is no pulmonary hypertension or congenital heart disease with left-to-right shunt.

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1. Arom KV, Richardson JD, Grover FL, Ferris G, Trinkle JK. Pulmonary artery aneurysm. Am Surg 1978;44(10):688-92.
2. Shih HH, Kang PL, Lin CY, Lin YH. Main pulmonary artery aneurysm. J Chin Med Assoc 2007;70(10):453-5.
3. Fernandes V, Kałuza GL, Zymek PT, DeFelice CA, Hust R, Raizner AE. Successful balloon valvuloplasty in an adult patient with severe pulmonic stenosis and aneurysmal poststenotic dilatation. Catheter Cardiovasc Interv 2002;55(3):376-80.
4. Tami LF, McElderry MW. Pulmonary artery aneurysm due to severe congenital pulmonic stenosis. Case report and literature review. Angiology 1994;45(5):383-90.
5. Shindo T, Kuroda T, Watanabe S, Hojo Y, Sekiguchi H, Shimada K. Aneurysmal dilatation of the pulmonary trunk with mild pulmonic stenosis. Intern Med 1995; 34(3):199-202.
6. Deterling RA Jr, Clagett OT. Aneurysm of the pulmonary artery; review of the literature and report of a case. Am Heart J 1947;34(4):471-99.
7. Chetty KG, McGovern J, Mahutte CK. Hilar mass in a patient with chest pain. Chest 1996;109(6):1643-4.
8. Bartter T, Irwin RS, Nash G. Aneurysms of the pulmonary arteries. Chest 1988;94(5):1065-75.
9. Decuypere V, Delcroix M, Budts W. Left main coronary artery and right pulmonary vein compression by a large pulmonary artery aneurysm. Heart 2004; 90(4):e21.
10. Smalcelj A, Brida V, Samarzija M, Matana A, Margetic E, Drinkovic N. Giant, dissecting, high-pressure pulmonary artery aneurysm: case report of a 1-year natural course. Tex Heart Inst J 2005;32(4):589-94.