Hakan ATALAR, Murat UÇAR, Tacettin AYANOĞLU, Osman Şahap ATİK, Ahmet Yiğit KAPTAN

Siringomiyeli'ye Bağlı Gelişen Charcot Omuz: Vaka Sunumu

Nöropatik atropati olarak da bilinen Charcot eklemi propriosepsiyon,ağrı ve sıcaklık duyusunun azaldığı yıkıcı bir hastalıktır. Diabetes mellitus, sirigomyeli ve tabes dorsalis gibi hastalıklar sonucu nöropatik atropati oluşabilir. Nöropatik artropati siringomiyeli olan hastaların %25 inde görülür ve bunların %80'i üst ekstremitede görülür. Ayırıcı tanıda septik artrit ve yumuşak doku sarkomuna mutlaka dikkat edilmelidir. Klinik olarak, nöropatik eklem hastalıkları ağrı ve hareket kısıtlılığı ile karakterize eklemde deformasyonla birliktedir. Siringomyeli süresince nöropatik eklem hasarı erken veya geç dönemde gelişebilir. Tedavi hedefleri fonksiyonel eklem hareket açıklığını korurken eklem hasarını azaltmak olmalıdır. Başlangıçta semptomatik tedavi içeren NSAİD, ortezler, ağırlık vermeyi azaltan teknikler ve hasta eğitimi gibi mekanik tekrarlayıcı travmayı azaltacak konservatif yöntemler uygulanmalıdır. Bu çalışmanın amacı daha önce birçok merkeze omuz ağrısı nedeniyle başvurup tanı alamayan siringomyeli tanılı bir hastanın klinik özellikleri ile birlikte radyolojik olarak görüntüleme bulgularını ortaya koymaktır.

Charcot Arthropaty Caused by Syringomyelia: Case Report

Charcot joint also known as neuropathic arthropathy is a disease that decreases the feeling of proprioception, pain and temperature sensation. Diabetes mellitus, syringomyeli and tabes dorsalis may be the cause of neuropathic arthropathy. Neuropathic arthropathy is seen among 25% of patients who are diagnosed syringomyeli, and 80% of patients' upper extremity are effected. The differential diagnosis and septic arthritis and soft tissue sarcomas should be made with caution. The majority of patients present symptoms of neuropathic pain and the limitation of motion. During syringomyelia joint damage can develop at the early or late period of the disease. Treatment goals should be to reduce the joint damage while maintaining the functional range of motion. Initially, NSAIDs, orthotics, techniques that reduce weight to the joint and the patient education to prevent repetative trauma should be prefered as consevative treatments. The purpose of this study is to reveal radiologic imaging findings with clinical features of a patient who can not be diagnosed before contacting many centers because of the shoulder pain diagnosed with syringomyelia.

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