Tahir Kurtuluş YOLDAŞ, Yıldız ÇORUH, Hava Dönmez KEKLİKOĞLUA, Hayriye Gül POLAT, Bülent GÜVEN

Hirayama Hastalığı (Monomelik Amyotrofi)

Hirayama Hastalığı (HH), genç erkeklerde daha sık görülen benign bir alt motor nöron hastalığıdır. Distal ekstremiteyi tutan ilerleyici güçsüzlük ve sinsi başlangıç ile karekterizedir. Genellikle başlangıcından sonra 5 yıl içinde stabilize olan, benign ve nonprogresif bir hastalık olarak kabul edilir. Biz bu bildiride duysal yakınmanın eşlik etmediği progresif amyotrofi bulguları olan 23 yaşında bir kadın hastayı sunuyoruz.©2008, Fırat Üniversitesi, Tıp Fakültesi

Anahtar Kelimeler:

Hirayama hastalığı, monomelik amyotrofi, motor nöron hastalığı

Hirayama Disease (Monomelic Amyotrophy)

Hirayama Disease (HD) is a benign lower motor neuron disorder in the young with male preponderance. It is characterized by insidious onset and progressive weakness and wasting of a distal extremity . Generally, this disease is considered a 'benign' and non-progressive motor neuron disease, which stabilizes within five years of onset.We describe a 23-year-old famele patient who experienced progressive amyotrophy with no sensorial abnormality.©2008, Firat University, Medical Faculty.

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Kabul Tarihi:22.11.2007