ÖZETPierre Robin sendromundan konjenitalkalp defektle-ri, iskeletsel anomaliler, g öz hasarları gibi sistemik bulgularda bulunmaktadır. Bununla birlikte, bu hastaların bir çoğunda zeka geriliği de görülebilmektedir. Doğumdan sonraki 5 yıl içinde biçimsiz dokular normale yakın ilişkilere getirilmeye çalışılır fakat dilin veya alveoler proçesin intrauterinbasınçla nekroze olduğu durumlarda iyileşme potansiyeli azalmaktadır. Pierre Robinolgusu sunulmuştur. Pierre Robİn anomalisi, mikrog-nati, glossoptosis.ABSTRACTOther systemic findings may also be present in the Pierre Robin syndrome, including congenital heart defects, other skeletal anomalies and oculer lesions. In addition mental retardation is present in a significant number of these patients. Catch-up growth in the 5 years after birth frequently restores the distorted tissues to near, normal relationships, but where intrauterine pressure necrosis oj the tongue or alveolar process has occured, the potential recovery reduced.In this article, a case report of Pierre Robin syndrome is presented who was diagnosed at birth and associated cleft palate has been treated through the intervening years and at present his orthodontic treatment is contiuing.Key words: Pierre Robin anomaly, mikrognathi, glossoptosis.