Creutzfeldt-Jakob Disease

Creutzfeldt-Jakob hastalığı en yaygın insan prion patolojidir. Biz bu olgu sunumunda hastalığın başlangıcı ve ilerlemesini sembolik olarak sunduk. Biz hastanın semptom ve tanısal işlemlerini bildirdik. Bunlar; ani gelişen konfüzyon ile gelen 82 yaşında erkek hasta, ajitasyon , kognitif bozulma ile birlikte hafıza bozukluğu, psikiyatrik belirtiler ve ölüme neden olacak koma ya götürecek nörolojik defisitlerin bulunması. Patolojik inceleme ile hastanın tanısı konuldu

Anahtar Kelimeler:

Pratisyen hekim, demans, Creutzfeldt-Jakob hastalığı

Creutzfeldt-Jakob Disease

Creutzfeldt-Jakob disease is the most common human prion pathology. The case report we describe is emblematic of this disease in its form of onset and progression. We have reported the symptoms and the diagnostic possibilities: a 82 years old man accused suddenly confusion, agitation, memory impairment with rapid progression of cognitive decline and psychiatric signs and the appearance of other neurological deficits that led the patient quickly to coma leading to death. Then, the pathological examination clarified the nature of patient's medical and it allowed players to make the diagnosis.

Keywords:

General practitioner, dementia, Creutzfeldt-Jakob disease,

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