ELÇİN AYDIN, Tülay ATASOY ÖZTÜRK, MEHMET ARGIN

Primer hiperoksalüri

Hiperoksalüri nefrolithiazis ve nefrokalsinozis ile karakterize, idrardaki kalsiyum oksalat/n süpersatürasyonu sonucu oluşur. Kalsiyum oksalat depozit/eri böbrek hasarı, böbrek yetmezliği ve diğer organlarda hasar/anmaya neden olabilir. Burada nadir de olsa ciddi bir durum arz eden, renal özellikleri açısından şüphelenilebilen primer hiperoksalüri vakasını sunduk. Radyolojik iskelet değişiklikleri oldukça spesifik olmakla birlikte renal osteodistrofi ile benzer özellikler taşıyabilir.

Primary hyperoxaluria

Hyperoxaluria is characterized by nephrolithasis and nephrocalcinosis caused by supersaturation of calcium oxalate in the urine. Deposits of calcium oxalate can lead to kidney damage, kidney failure, and injury to other organs. Herein, we report case of primary hyperoxaluria which is serious though rare condition, can be suspected on the basis of the renal features. Radiological skeletal changes, which are also rather specific, may also share some features with renal osteodystrophy.

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