Gülden DİNİZ, Ragıp ORTAÇ, Safiye AKTAŞ, Günyüz TEMİR, MÜNEVVER HOŞGÖR, İrfan KARACA

Göğüs duvarı hamartomu: Olgu sunumu

Göğüs duvarı hamartomu saptanan 4 aylık kız bebek sunulmuştur. Yenidoğan ve infantlarda oldukça nadir görülen bu karakteristik lezyon ; salt kitle varlığıyla tanınabileceği gibi basıya bağlı respiratuvar semptomlara yol açabilir. Spontan regresyon bildirmiştir. Günümüzde asemptomatik olgularda konservatif yaklaşım yeğlenmektedir. Ender görülmesine karşın klinik olarak malignite kuşkusu doğurabileceği için ; çocukluk çağı toraks tümörlerinin ayırıcı tanısında akılda tutulmalıdır. Burada lezyonu diğer malign ve benign neopiazmiardan ayıran histopatolojik özellikler irdelenmiştir.

Anahtar Kelimeler:

Toraks duvarı, Çocuk, Tanı, ayırıcı, Hamartom

Chest wall hamartoma: Case report

A case of four-month - old girl diagnosed as chest wall hamartoma is presented. This entity is an extremely rare but characteristic lesion of the ribs usually presenting in the neonate or infant with a mass or respiratory symptoms. Complete sponraneous regression of the lesion has been reported. Recently conservative management of asymptomatic childiren was recommended. Although rare, this condition ought to be kept in mind while dealing with infantile chest wall masses to avoid an erroneous diagnosis of malignancy. It has to be distinguished from benign and malignant neoplasms on the basis of distinct histological features discussed here.

Keywords:

Thoracic Wall, Child, Diagnosis, Differential, Hamartoma,

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1. A M Freeburn, J McAloon Infantile chest hamartoma case outcome aged 11. Arch Dis Child 2001 ;85:244-245.
2. Rao L, Kini AC, Valiathan M, Gurpur CR, Rao RV. Infantile cartilaginous hamartoma of the rib. A case report. Acta Cytol. 2001;45(1):69-73.
3. Golla S, Wit J, Guschmann M, Lubbert E, Kerner T. Rare mesenchymal lesions: Hamartoma of the chest wall and juvenile active ossifying fibroma in siblings. J Pediatr Surg. 2002;37(9):E27.
4. McDermott MB, Ponder TB, Dehner LP. Nasal chondromesenchymal hamartoma: an upper respiratory tract analogue of the chest wall mesenchymal hamartoma. Am J Surg Pathol.1998; 22(4):425-33.
5. Watt AJ. Chest wall lesions. Paediatr Respir Rev. 2002; 3(4):328-38.
6. Shamberger RC, Grier HE. Chest wall tumors in infants and children. Semin Pediatr Surg. 1994; 3(4):267-76
7. Gore 0, Kilicalp A, Basdemir G, Özer E, Aktug T. Cartilaginous hamartoma of the chest wall with secondary aneurysmal cyst-like areas^in an infant: a case report. Turk J Pediatr. 1999;41(1): 139-42
8. Serrano-Egea A, Santos-Briz A, Garcia-Munoz H, Martinez-Tello FJ. Chest wall hamartoma. Report of two cases with secondary aneurysmal bone cysts. Pathol Res Pract. 2001; 197(12):835-9.
9. Groom KR, Murphey MD, Howard LM, Lonergan GJ, Rosado-De-Christenson ML, Torop AH. Mesenchymal hamartoma of the chest wall: radiologic manifestations with emphasis on cross-sectional imaging and histopathologic comparison. Radiology. 2002; 222(1 ):205-11.
10. Cameron D, Ong TH, Borzi P. Conservative management of mesenchymal hamartomas of the chest wall. J Pediatr Surg. 2001; 36(9): 1346-9.