Restriktif Kardiyomiyopati ve orta serebral arter infarkt birlikteligi: Vaka sunumu

Restriktif Kardiyomiyopati çocukluk çagindan oldukça nadir olarak karsimiza çikmaktadir. Tanimlanan kardiyomiyopatilerin ancak %5’ini olusturmaktadir ve prognozu oldukça kötüdür. Bu tür olgularda tromboza egilim ve tromboembolik durumlarin sikligi artmistir. Literatürde Restriktif Kardiyomiyopati ve orta serebral arter infarkti birlikteligi oldukça nadir bildirilmistir. Burada sol hemiparazi bulgulari ile basvuran nadir bir olgu sunularak, bu tip kardiyomiyopatili hastalarda tromboz ve tromboembolik olaylara dikkati çekmek istedik

Association of Restrictive Cardiomyopathy and Middle Cerebral Artery Infarct: A case report

Restrictive cardiomyopathy is rare in children, constituting 5% of diagnosed cardiomyopathies. Prognosis for the pediatric patient is poor. Thrombosis, embolic events are increased. Restrictive cardiomyopathy with middle cerebral artery infarct is rarely reported. We aimed to report Restrictive cardiomyopathy with middle cerebral artery infarct to explain thrombosis and thromboembolic events in Restrictive cardiomyopathy

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1. Lewis AB: Clinical profile and outcome of restrictive cardiomyopathy in children. Am Heart J. 123:1589-1593,1992.

2. Denfield SW, Rosenthal G, Gajarski RJ, Bricker JT, Schowengerdt KO, Price JK, Towbin JA: Restrictive cardiomyopathies in childhood. Etiologies and natural history. Tex Heart Inst J. 24:38-44,1997.

3. Ishijima M, Kawai S, Okada R, Ino T, Yobuta K: An autopsy case of cardiomyopathy with restrictive physiology in a child. Heart Vessels Suppl. 5:70-73,1990.

4. Cetta F, O'Leary PW, Seward JB, Driscoll DJ: Idiopathic restrictive cardiomyopathy in childhood: diagnostic features and clinical course. Mayo Clin Proc. 70:634-640,1995.

5. Rivenes SM, Kearney DL, Smith EO, Towbin JA, Denfield SW: Sudden death and cardiovascular collapse in children with restrictive cardiomyopathy. Circulation. 102:876-882,2000.

6. Russo LM, Webber SA: Idiopathic restrictive cardiomyopathy in children. Heart. 91:1199-1202,2005.

7. Denfield SW: Sudden death in children with restrictive cardiomyopathy. Card Electrophysiol Rev. 6:163- 167,2002.

8. Gewillig M, Mertens L, Moerman P, Dumoulin M: Idiopathic restrictive cardiomyopathy in childhood. A diastolic disorder characterized by delayed relaxation. Eur Heart J. 17:1413- 1420,1996.

9. Park MK, Trexler RG: Restrictive Cardiomyopathy. In Park MK, Trexler RG: Pediatric Cardiology for Practitioners St. Louis: Mosby. pp:279- 280,2002.

10. Weller RJ, Weintraub R, Addonizio LJ, Chrisant MR, Gersony WM, Hsu DT: Outcome of idiopathic restrictive cardiomyopathy in children. Am J Cardiol. 90:501-506,2002.

11. Chen SC, Balfour IC, Jureidini S: Clinical spectrum of restrictive cardiomyopathy in children. J Heart Lung Transplant. 20:90-92,2001.

12. Kimberling MT, Balzer DT, Hirsch R, Mendeloff E, Huddleston CB, Canter CE: Cardiac transplantation for pediatric restrictive cardiomyopathy: presentation, evaluation, and short-term outcome. J Heart Lung Transplant. 21: 455-459,2002