Nilgün EROĞLU, Mustafa POLAT, ALİ AYKAN ÖZGÜVEN, Şenol COŞKUN

Nörolojik sekel bırakmayan hemorajik şok ensefalopati sendromlu bir olgu

Hemorajik şok ensefalopati sendromu süt çocukluğu döneminde ani olarak başlayan şok, ensefalopati, dissemine intravasküler koagülasyon, metabolik asidoz ve çoklu organ yetmezliği ile giden, nadir görülen bir tablodur. Nedeni bilinmeyen bu sendromun mortalite ve nörolojik morbidite oranı oldukça yüksektir. Hemorajik şok ensefalopati sendromu tanısı konulduktan sonra nörolojik sekelsiz iyileşen 9 aylık bir olgu literatürler eşliğinde tartışıldı.

A case of hemorrhagic shock and encephalopaty syndrome without neurological sequel

Hemorrhagic shock and encephalopathy syndrome is a severe disease that affect infants of less than 1 year of age and characterized by sudden onset of shock, encephalopathy, disseminated intravascular coagulation, metabolic acidosis and multiple organ dysfunction. The etiology of this syndrome is unknown and is associated with significant mortality and neurologic morbidity. We discussed a case of hemorrhagic shock and encephalopathy syndrome aged 9 months who recovered without neurologic morbidity and also the literature related with this syndrome was reviewed.

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