Yılmaz YOZGAT, Gizem SARI, Emre ÖTEYAKA, Mehmet Turan BASUNLU, Okan Eren KUĞUOĞLU, Can Yılmaz YOZGAT, Didem Melis ÖZTAŞ, Mehmet Sait DOĞAN, Murat UĞURLUCAN, Halil TÜRKOĞLU

Aortik Kros Klemp ile Myokard İskemisi Yaratmadan Konjenital Düzeltilmiş Büyük Arter Transpozisyonlu Asendan Aortu Hipoplazik Tip A Kesintili Aortik Arkı Olan Hastanın Tedavisi

İnterrupted aortik ark tedavisi karmaşık bir süreçtir. Cerrahi rekonstrüksiyon genellikle myokard iskemisine neden olan aortik kros klempleme, kalbin durdurulması ve hatta kansız operasyon sahası için derin hipotermi gerektirir.Bu yazıda, normotermik şartlarda, kalbi durdurmadan çıkan aort, aortik ark ve proksimal desendan aort replasmanını selektif kanülasyon ve tüm vücut perfüzyonunu sağlayan cerrahi teknik ile tedavi ettiğimiz konjenital düzeltilmiş büyük arter transpozisyonu, tip A kesintili aortik ark ve hipoplazik asendan aortu olan hastamızı sunuyoruz. Anahtar Kelimeler: Arkus aorta, Kesinti, Konjenital düzeltilmiş büyük arter transpozisyonu, Kanülasyon. ABSTRACT Treatment of interrupted aortic arch is complex. Surgical reconstruction consists of procedures that cause myocardial ischemia, such as aortic cross clamping, cardioplegia, and hypothermia. In this article, we present a patient with congenitally corrected transposition of great arteries together with Type A interruption as well as hypoplastic ascending aorta and the aortic arch. The replacement of the aorta, aortic arch, and the proximal descending aorta was performed under normothermic conditions without cardioplegia, which was achieved with a technique that preserves the systemic blood supply by using selective cannulation. Aortic Arch, Interruption, Congenitally corrected transposition of great arteries, Cannulation.

Anahtar Kelimeler:

Aortic Arch, Interruption, Congenitally corrected transposition of great arteries, Cannulation.

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