Nadir görülen bir böbrek tümörü: Müsinöz tübüler ve iğsi hücreli karsinom

Müsinöz tübüler ve iğsi hücreli karsinom yakın geçmişte tanımlanmış, nadir görülen bir böbrek tümörüdür. Literatürde tek olgu veya küçük olgu serileri şeklinde bildirilmiş- tir. Tümör düşük dereceli, rölatif olarak iyi prognozludur. Burada nadir görülen olgumuzu klinikopatolojik özellikleriyle ve patojik ayırıcı tanısıyla sunduk.

A rare kidney neoplasm: Mucinous tubular and spindle cell carcinoma

Mucinous tubular and spindle cell carcinoma has recently been recognized as a rare tumor of the kidney. Single cases or small series have been reported in the literature. The tumor is considered to be a low-grade carcinoma with a relatively favorable prognosis. Here we presented our rare case with clinicopathologic features and pathological differential diagnosis.

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  • 1. Srigley JR: Mucinous tubular and spindle cell carcinoma. In Tumours of the Urinary System and Male Genital Organs. World Health Organization Classification of Tumours. Edited by Eble JN, Sauter G, Epstein JI, Sesterhenn IA. Lyon, France:IARC Press; 2004:40.
  • 2. Lima MS, Barros-Silva GE, Pereira RA, et al.The imaging and pathological features of a mucinous tubular and spindle cell carcinoma of the kidney: a case report. World J Surg Oncol 2013 ;2:11-34.
  • 3. Chrysikos D, Zagouri F, Sergentanis TN, et al. Mucinous tubular and spindle cell carcinoma of the kidney: a case report. Case Rep Oncol 2012;5:347-353.
  • 4. Jung SJ, Yoon HK, Chung JI et al. Mucinous tubular and spindle cell carcinoma of the kidney with neuroendocrine differentiation: report of two cases. Am J Clin Pathol 2006;125:99-104.
  • 5. Hes O, Hora M,Perez-Montiel DM, et al. Spindle and cuboidal renal cell carcinoma, a tumour having frequent association with nephrolithiasis: report of 11 cases including a case with hybrid conventional renal cell carcinoma/spindle and cuboidal renal cell carcinoma components. Histopathology 2002;41:549-555.
  • 6. Ferlicot S, Allory Y, Comperat E, et al. Mucinous tubular and spindle cell carcinoma: a report of 15 cases and a review of the literature. Virchows Arch 2005;447:978-983.
  • 7. Sarsık B, Şimşir A, Karaarslan S, Şen S. Mucinous tubular and spindle cell carcinoma of kidney and problems in diagnosis. Türk Patoloji Derg 2011;27:116-126.
  • 8. Farghaly H. Mucin poor mucinous tubular and spindle cell carcinoma of the kidney, with nonclassic morphologic variant of spindle cell predominance and psammomatous calcification. Ann Diagn Pathol 2012;16:59-62.
  • 9. Pillay N, Ramdial PK, Cooper K, Batuule D. Mucinous tubular and spindle cell carcinoma with aggressive histomorphology--a sarcomatoid variant. Hum Pathol 2008;39:966- 969.
  • 10. Owens CL, Argani P, Ali SZ. Mucinous tubular and spindle cell carcinoma of the kidney: cytopathologic findings. Diagn Cytopathol 2007;35:593-596.
Dicle Tıp Dergisi-Cover
  • ISSN: 1300-2945
  • Yayın Aralığı: 4
  • Başlangıç: 1963
  • Yayıncı: Cahfer GÜLOĞLU
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