İLYAS YOLBAŞ, Selvi KELEKÇİ, Yusuf Kenan HASPOLAT, ALİ GÜNEŞ, VELAT ŞEN

Large congenital cystic asdenomatous malformation of the lung in a newborn

Akciğerin konjenital kistik adenoid malformasyonu akciğerin hava ile dolu kistlerinden oluşan bir hemartöz lezyondur. Genelde doğumdan sonra solunum sıkıntısı ile bulgu verir. Konjenital pnömoni, respiratuvar distress sendromu ile ayırıcı tanısı zordur. Doğumdan sonra şiddetli solunum sıkıntısı ve düşük Apgar olan bir erkek yenidoğan entübe edildikten sonra yenidoğan yoğun bakım ünitemize yatı- rıldı. Hasta 50 gün mekanik ventilatörde takip edildikten sonra 50. gün mekanik ventilatörden ayrıldı. Tip II Akciğerin konjenital kistik adenoid malformasyonu tanısı akciğer tomografisi ve akciğer grafi bulguları ile kondu. Cerrahi lobektomi önermesine rağmen hastanın tümüyle aseptomatik olmaması ve ölüm riski nedeniyle aile operasyonu kabul etmedi. Hasta kontrole gelmek üzere taburcu edildi.

Yenidoğanda akciğerin büyük konjenital kistik adenomid malformasyonu

Congenital cystic adenomatous malformation (CCAM) of lung is a rare form of congenital hamartomatous lesions of the lung consisting of cysts filled with air. The general clinic presentation of CCAM is dyspnea in newborns. CCAM may mimic congenital pneumonia or respiratory distress syndrome. After the delivery, the newborn male who had low Apgar score and severe respiratory distress was intubated and admitted to neonatal intensive care unit. Patient was ventilated for 50 days and weaned from the mechanical ventilator at 50th day. Type II CCAM of the lung was diagnosed according to the chest radiographs and computed tomography scan signs. Although the surgeons suggested lobectomy considering the patients not completely asymptomatic, family did not accept this operation due to the risk of death. The patient was discharged from the hospital until the next control.

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