Şakir ALTUNBAŞAK, Faruk İNCECİK, Özlem M HERGÜNER, Gülen Gül MERT, Fatma Derya BULUT

Tekrarlayan Fasiyal Paralizili bir Olgu: Melkersson Rosenthal Sendromu

Melkersson-Rosenthal sendromu (MRS), tekrarlayan fasiyal paralizi, orofasiyal ödem, dilde fissürle karakterize nadir bir nöromukokütanöz sendromdur.Oligosemptomatik ve monosemptomatik olgular, klasik triaddan sık görülür.Bulguların ikisinin görülmesi veya bulguların biri ve biyopside granülomatöz keilitin varlığı Melkersson-Rosenthal sendromu tanısı için yeterlidir. Bu yazıda Melkersson-Rosenthal sendromu tanısı alan 12 yaşında bir erkek sunulmuştur.

A Case with Recurrent Facial Palsy: Melkersson-Rosenthal Syndrome

Melkersson-Rosenthal syndrome (MRS) is a rare neuromucocutaneous syndrome characterized by reccurent facial paralysis, orofacial edema and fissured tongue. Oligosymptomatic and monosymptomatic forms are more common than the triad. The presence of two manifestations or one manifestation with granulomatous cheilitis in biopsy is sufficient to make diagnosis of Melkersson-Rosenthal syndrome. We present a 12 years-old male who is diagnosed MelkerssonRosenthal syndrome.

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