Anesthetic Approach to a Child with Noonan's Syndrome

Noonan Sendromu konjenital kalp hastalıkları ile birlikte yüz ve fiziksel özellikler ile tanımlanır. Bu hastalar yüz anomalileri olarak kısa yele boyun, mikrognati, yüksek damak ve sınırlı ağız açıklığı içermektedir. Pulmoner stenoz ve hipertrofik obstüktif kardiyomyopati Noonan Sendromunda yüksek oranda görülmektedir. Zor havayolu ve ciddi kardiyak anomaliler nedeniyle anestezi yönetimi önem taşımaktadır. Bu makalede Noonan Sendromlu bir çocukta anestezi yönetimi sunulmuştur.

Noonan Sendromlu Bir Çocukta Anestezik Yaklaşım

Noonan syndrome is characterized by fascial and physical features with congenital heart disease. In these patients, fascial features include short webbed neck, micrognathia, limited mouth opening and high arched palate. Pulmonary stenosis and hypertrophic obstructive cardiomyopathy are highly prevalent in Noonan's syndrome. The anesthetic management is important because of difficult airway and severe cardiac abnormalities. We reported that anesthetic management of a child with Noonan's syndrome.

___

  • Macksey LF, White B. Anesthetic management in a pediatric patient with Noonan syndrome, mastocytosis, and von Willebrand disease: a case report. AANA J. 2007;75:261-4.
  • Bertola DR, Kim CA, Sugayama SM, Albano LM, Wagenführ J, Moysés RL et al. Cardiac findings in 31 patients with Noonan's syndrome. Arq Bras Cardiol. 2000;75:409-12.
  • Schwartz N, Eisenkraf JB. Anesthetic Management of a Child With Noonan's Syndrome and Idiopathic Hypertrophic Subaortic Stenosis. Anesth Analg. 1992;74:464-6.
  • Karaman A, Keskin H, Kaçmaz E, Laloğlu F, Ömeroğulları Z. Noonan sendromu: Olgu sunumu. Göztepe Tıp Dergisi. 2013;28:48-50.
  • Chase CJ, Holak EJ, Pagel PS. Anesthetic implications of emergent Cesarean section in a parturient with Noonan syndrome and bacterial endocarditis. J Clin Anesth. 2013;25:403-6.
  • Aggarwal V, Malik V, Kapoor PM, Kiran U. Noonan syndrome: An anesthesiologist's perspective. Ann Card Anaesth 2011;14:214-7.
  • Dahl V, Pendeville PE, Hollmann MW, Heier T, Abels EA, Blobner M. Safety and efficacy of sugammadex for the reversal of rocuronium-induced neuromuscular blockade in cardiac patients undergoing noncardiac surgery. Eur J Anaesthesiol. 2009;26:874-84.
  • Tüfek A, Yildirim B, Tokgöz O, Karaman H, Celik F, Aycan IO. Immediate cardiac arrest after neostigmine administration. J Pak Med Assoc. 2012;62:609-11.
Çukurova Üniversitesi Tıp Fakültesi Dergisi-Cover
  • ISSN: 0250-5150
  • Yayın Aralığı: 4
  • Yayıncı: Tülay Candan