Feride KARACAER, Ersel GÜLEÇ, Dilek ÖZCENGİZ, Ebru BİRİCİK, Özgür SÜRMELİOĞLU

Amyloidosis and difficult airway: a case report

Amiloidozis, moleküllerinin ekstrasellüler birikimi ile karakterize bir hastalıktır. Amiloid birikimi kalp, karaciğer, böbrek, cilt, barsak, otonom sinir sistemi, dil ve karpal tünelde görülebilir. Dilde amiloidozis, amiloidin suprahyoid kaslarda ekstrasellüler depozisyonuna bağlı makroglossi çoğunlukla görülmektedir.Anestezistler amiloidozisle pek çok farklı durumda karşılaşabilirler. Dilde amiloid birikimine bağlı zor hava yolu beklenmedik bir durumdur. Fiberoptik bronkoskopi ile acil trakeostomi açılmasını sağladık ve herhangi bir komplikasyon gözlenmedi. Burada amiloidozise bağlı aşırı büyük dilden kaynaklanan solunum sıkıntısını sunulması amaçlanmıştır

Amiloidozis ve zor hava yolu: olgu sunumu

Amyloidosis is a disease which can affect any tissue in the body with extracellular deposition of low molecular weight protein fibrils. Amyloid deposition can appear in many organs and tissues. Amyloidosis of tongue occurs most commonly in systemic form as rubbery macroglossia due to extra-deposition of amyloid within the suprahyoid muscle. Anesthesiologist can experience the negative consequences of amyloidosis in many conditions. Difficult airway due to amyloid deposition in tongue is an unexpected condition. We aimed to report a case that had respiratory distress with extremely big tongue due to amyloidosis. We performed a fiberoptic intubation for emergent tracheostomy without any complication

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