İntrakraniyal Kitleyi Taklit Eden Tumefaktif Multipl Skleroz Olgusu

Tümefaktif multiple skleroz fokal serebral kitle olarak prezante olan nadir bir demiyelinizan hastalıktır. Klinik ve radyolojik olarak genellikle tümör veya apseden ayrımı zordur. Ayırıcı tanıda eğer şüphe varsa invazif girişimlerden önce görsel uyarılmış potansiyeller ve BOS analizi yapılması, yüksek doz kortikosteroid tedavisi denenmesi önerilmektedir. Bu yazıda sol hemiparezi ile başvuran, radyolojik olarak lezyonu kitle lezyonu olarak değerlendirilip gross total tümör eksizyonu uygulanmış ancak patoloji sonucu demiyelinizan hastalık ile uyumlu gelen 13 yaşında bir kız hasta sunulmuştur. Tümefaktif multipl skleroz, multipl skleroz, fokal serebral lezyon

Anahtar Kelimeler:

Tümefaktif multipl skleroz, multipl skleroz, fokal serebral lezyon

A Tumefactive Multiple Sclerosis Case Mimicking a Focal Cerebral Mass

Tumefactive multiple sclerosis is a rare demyelinating disease presenting with a focal cerebral mass. Clinically and radiographically, the disease is usually difficult to differentiate from a tumor and abscess. If there is a doubt in the differential diagnosis, visual evoked potentials and CSF analysis and a trial with high dose corticosteroids should contribute to the evaluation of the patient before invasive procedures are started. Here we present a 13 year old girl with left hemiparesis, and a mass lesion on imaging studies confused with a tumor. Gross total tumor excision was performed. The pathology was consistent with a demyelinating disease.

Keywords:

Tumefactive multiple sclerosis, multipl sclerosis, focal cerebral lesion,

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