Erişkinlerde Baş ve Boyun Lenfanjiomları: Tek Merkez Deneyimi

Amaç: Hastanemizde cerrahi rezeksiyon uygulanan erişkin baş boyun lenfanjiomlarının klinikopatolojik özelliklerini ortaya koymayı amaçladık. Materyal ve Metod: 2008-2020 yılları arasında laboratuvarımızda incelenen 18 yaş üstü hastaların baş boyun bölgesinden yapılan tüm cerrahi rezeksiyon materyalleri retrospektif olarak incelendi. Lenfanjiyom tanısı konulan olgular çalışmaya dahil edildi. Bulgular: Çalışmaya dahil edilen 34 lenfanjiomdan 17'si kadın, 17'si erkekti. Hastaların yaşları 19 ile 76 arasında değişmekteydi. Medyan lenfanjiyom boyutu 0.8 cm idi. Lezyonlar 15 (% 44,1) hastada yüzde, dokuz (% 26,5) hastada ağız boşluğunda, altı (% 17,6) hastada boyunda, üç hastada (% 8,8) orbital ve perioküler bölgede, bir hastada (%2,9) kulakta lokalize idi. Lenfanjiyomların 16'sı (%47,0) lenfanjiyoma sirkumscriptum, 14'ü (%41,2) kavernöz lenfanjiyom ve dördü (%11,8) kistik lenfanjiyom olarak tanımlandı. 1.5 cm'den büyük tüm lezyonlar boyun veya ağız boşluğunda yerleşmişti. Ağız boşluğundaki tüm lezyonlara kavernöz lenfanjiom tanısı konuldu. Dört kistik lenfanjiomun tamamı boyunda tespit edildi. Lenfanjiom iki olguda nüksetti; malign transformasyon saptanmadı. Sonuç: Baş boyun lenfanjiyomları erişkinlerde nadir değildir, her yaşta görülebilirler. Kistik lenfanjiomlar sıklıkla boyunda ve kavernöz lenfanjiomlar ağız boğluğunda görülür. Total cerrahi rezeksiyon hem tedavi hem de kesin tanı sağlar. Nüks görülebilir ancak malign transformasyon beklenmez.

Anahtar Kelimeler:

lenfanjiyom, baş ve boyun, kavernöz lenfanjiyom, kistik lenfanjiyom, lenfanjiyoma sirkumskriptum, vasküler malformasyon

Head and Neck Lymphangiomas in Adults: A Single Center’s Experience

Aim: We aimed to reveal the clinicopathologic features of adult head and neck lymphangiomas that underwent surgical resection in our hospital. Material and Method: All surgical resection materials of patients aged older than 18 years from the head and neck region that were examined at our labaratory between 2008 and 2020 were retrospectively reviewed. Cases diagnosed as lymphangioma were included in the study. Results: Of the 34 lymphangiomas included in the study, 17 were from females and 17 from males. The ages of the patients ranged between 19 and 76 years. The median lymphangioma size was 0.8 cm. Lesions were located on the face in 15 (44.1%) patients, in the oral cavity in nine (26.5%), on the neck in six (17.6%), on the orbital and periocular region in three (8.8%), and on the ear in one (2.9%) patient. Of the lymphangiomas, 16 (47.0%) were defined as lymphangioma circumscriptum, 14 (41.2%) as cavernous lymphangioma, and four (11.8%) as cystic lymphangioma. All lesions larger than 1.5 cm were located in the neck or oral cavity. All lesions in the oral cavity were diagnosed as cavernous lymphangioma. All four cystic lymphangiomas were identified in the neck. Lymphangioma recurred in two cases; no malignant transformation was detected. Conclusion: Head and neck lymphangiomas are not uncommon in adults, they can be seen at any age. Cystic lymphangioma is often seen in the neck and cavernous lymphangioma in the oral cavity. Total surgical resection provides both treatment and definitive diagnosis. Recurrence can be seen, but malignant transformation is not expected.

Keywords:

lymphangioma, head and neck, cavernous lymphangioma, cystic lymphangioma, lymphangioma circumscriptum, vascular malformation,

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