Ön Boynuz Tutulumuyla Giden Hastalıklar

Ön boynuz motor nöronlar, spinal korddan çıkan uyarıları aksiyel kaslara taşıyan yolaklardır. Ön boynuz motor nöronlarının hastalıklarında ortak olarak lezyon seviyesinde gevşek parezi veya paralizi, kısmi veya tam refleks kayıpları ve kaslarda atrofi ortaya çıkar. Bu hastalıklar duyu kaybına sebep olmazlar, ama ölümcül seyredebilirler, tedavileri çoğunlukla destek tedavisidir, semptomatik tedaviler yaşam kalitesini artırmak için uygulanabilir. Bu derlemede ön boynuz hastalıkları, tanı kriterleri ve yönetimi ayrıntılı olarak tartışılmıştır.

Anterior Horn Cell Diseases

The anterior horn cells control all voluntary movement. Motor activity, respiratory, speech, and swallowing functions are dependent upon signals from the anterior horn cells. Diseases that damage the anterior horn cells, therefore, have a profound impact. Symptoms of anterior horn cell loss (weakness, falling, choking) lead patients to seek medical attention. In this article, anterior horn diseases were reviewed, diagnostic criteria and management were discussed in detail.

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