Fulya YILMAZ, Burcu ULUGÖLGE

General anesthesia management with laryngeal mask airway in a patient with epidermolysis bullosa: Case report

Yayın Aralığı: 12
Yayıncı: İnönü Üniversitesi Tıp Fakültesi

Epidermolysis bullosa (EB) is a rare (1/17000-1/300000) genetic disease which is characterized by an abnormal collagen and extremefragility of skin and mucous membranes. We report successful management of a 24-year-old-woman with epidermolysis bullosapresented to operation room for local resection of mass on tuberositas tibia under general anesthesia with laryngeal mask airway.Anesthesia management of EB cases requires features at all stages of anesthesia management. A multidisciplinary approach andcareful planning are essential for safely management of surgery.

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1. Araújo M, Brás R, Frada R, et al. Caesarean delivery in a pregnant woman with epidermolysis bullosa: anaesthetic challenges. Int J ObstetAnesth 2017;30:68-72.
2. Strupp KM, Zieg JA, Johnson B, et al. Anesthetic Management of a Patient With Epidermolysis Bullosa Requiring Major Orthopedic Surgery: A Case Report. Anesth Analg 2017;9:73-6.
3. Bowen L, Burtonwood MT. Anaesthesic management of children with epidermolysis bullosa. BJ A Education 2018;18:41-5.
4. Saraf SV, Mandawade NJ, Gore SK, et al. Epidermolysisbullosa: Careful monitoring and no touch principle for anesthesia management. J Anaesthesiol Clin Pharmacol 2013;29:390-3.
5. Nandi R, Howard R. Anesthesia and Epidermolysis Bullosa. DermatolClin 2010;28:319-24.
6. Ames WA, Mayou BJ, Williams K. Anaesthetic management of epidermolysis bullosa. Br J Anaesth 1999;82:746-51.