Dermatofibrosarcoma protuberans: An unusual case of breast

Dermatofibrosarcoma protuberans (DFSP) is a rare tumor of the breast. It is locally aggressive tumor with high rate of local recurrences.A 64 years-old female patient had recurrent large two DFSP lesions in left breast 14 months after the segmental mastectomy. Nodistant metastasis was detected. The patient underwent mastectomy. She refused adjuvant treatment. Despite wide resection wasperformed in the second surgery, the disease recurred again. As a conclusion, unless effective adjuvant treatments and medicationsare not present, surgical excision is crucial to prevent recurrence.

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