Hüseyin DİNDAR, Selim EREKUL, Okçu Aylin HEPER, Küpana Şebnem AYVA

Soliter kutanöz mastositoma

Mastositozis, mast hücrelerinin anormal proliferasyonu ve mast hücre mediatörlerinin salınımı ile karakterli, kutanöz veya sistemik, az görülen, heterojen bir grup hastalıktır. Klinik gidiş benign veya agresif olabilmektedir. Kutanöz mastositozisin tanısı için klinik bulgular ile birlikte mast hücrelerinin dermal infiltrasyonunun histopatolojik olarak gösterilmesi gerekmektedir. Kutanöz mastositozis, akla getirilmesi halinde, her türlü laboratuar şartları altında uygulanabilecek ve basit histokimyasal boyalarla tanısı çok kolay konabilecek bir antitedir. Burada çocuk yaş grubuna ait soliter kutanöz mastositoma olgusunun histolojik özellikleri, literatür bilgileri eşliğinde sunulmaktadır.

Solitary cutaneous mastocytoma

Mastocytosis is a rare cutaneous or a systemic heterogenous group of disease characterized by abnormal proliferation of mast cells and the release of mast cells' mediators. The clinical outcome may be benign or aggressive. For the diagnosis of cutaneous mastocytosis, dermal infiltration of mast cells must be shown histopathologically in addition to clinical findings. Cutaneous mastocytosis is an entity in which the diagnosis can be made so easily in every laboratory conditions with simple histochemical stains. In this case report, the histological features of a solitary cutaneous mastocytoma in a pediatric age group is presented with a review of literature.

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