Karın İçi Kistik Kitle ve Obstrüktif Üropati ile Başvuran İki Yenidoğan: Vajinal Atreziye Bağlı Hidrometrokolpos

Vajinal atrezi nadir görülen bir doğumsal anomalidir ve tedavi yaklaşımları genellikle semptomlara bağlı olarak çeşitlilik gösterir. İntraabdominal kistik kitle ve obstrüktif üropati ile başvuran vajinal atrezi tanılı iki yenidoğan sunuldu. Fizik muayenelerinde palpasyonla umblikus üzerine uzanan kitlesel lezyon mevcuttu ve vajen açıklığının olmadığı görüldü. El ve ayaklarda polidaktili vardı. Her iki hastaya da abdominoperineal yaklaşımla vajinoplasti yapıldı. Hastalar halen ameliyat sonrası 2. yılında olup takipleri sorunsuzdur. Karın içi kistik kitle ve polidaktili bulguları olan hastalarda vajinal atrezi ve hidrometrokolpos akla gelmelidir.

Two Newborns Presenting with Intraabdominal Cystic Mass and Obstructive Uropathy: Hydrometrocolpos due to Vaginal Atresia

Vaginal atresia is a rare congenital anomaly and treatment approaches are varied, usually driven by symptoms. We report two newborns presenting with an intraabdominal cystic mass and obstructive uropathy due to vaginal atresia. Physical examination revealed a mass lesion extending to the umbilicus and lack of vaginal patency. They had polydactyly on hands and feet. Both patients underwent vaginoplasty with abdominoperineal approach. The patients are still in the 2nd postoperative year and their follow-up is uneventful. Vaginal atresia and hydrometrocolpos should be considered in patients with intraabdominal cystic mass and polydactyly findings.

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