Günay EKBERLİ, aydın YAĞMURLU, Nil Yaşam TAŞTEKİN, Gülnur Göllü BAHADIR, Ufuk ATEŞ

Fanconi Aplastik Anemisi ve Transvers Vajinal Septum Birlikteliği

Fanconi aplastikanemisi birçok konjenital anomalinin eşlik ettiği genetik kökenli defektif hematopoezdurumu-- dur. Genitoüriner sistem anomalileri %20 oranında eşlik eder. Literatürde genitoüriner anomali olarak transvers vajinal septum ve Fanconi aplastik anemi birlikteliğine rastlanmamıştır. Konjenital transvajinal septumun eşlik ettiği 13 yaşında Fankoni aplastik anemili hastanın sunumu ve yaklasımımızın aktarılması amaçlandı.

Concominitance of Fanconi Aplastic Anemicı with Transverse Vaginal Septum

Fanconi anemia is genetic defective hematopoesis condition characetrised by multipl congenital anomalies. Concomitance of genitourinary anomalies are 20%. There is lack of literature about concomitance of Fanconi anemia and transverse vaginal septum as genitourinary anomalie. in this article, 13-year old Fanconi aplastic anemia patient with vaginal septum and our approach aimed to be reported.

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