Ersel DAĞ, Yakup TÜRKEL, Murat ALPUA, Yasin HABİPOĞLU, Ahmet ADIGÜZEL

ABSANS NÖBET İLE BAŞVURAN DYKE DAVİDOFF MASSON SENDROMU OLGUSU

Dyke Davidoff Mason Sendromu(DDMS) serebral hemiatrofinin mevcut olduğu hemiparezi ve rekürren epileptik nöbetlerle karakterize bir sendromdur. Biz de absans nöbetlerle prezente olan kranyal MR'ında hemisferik atrofinin mevcut olduğu tipik bir DDMS olgusu sunmak istedik. Olgunun çekilen elektroensefalografisinde jeneralize 3 Hz diken dalga deşarjları izlendi. Hastanın takibinde uygun antiepileptik tedavi ile nöbetleri kontrol altına alındı

DYKE DAVIDOFF MASSON SYNDROME PRESENTING WITH ABSENCE SEIZURES

Dyke-Davidoff-Masson syndrome (DDMS) consist of cerebral hemiatrophy and ipsilateral skull thickening, and is manifested by hemiparesis and recurrent seizures. We present one case with typical DDMS which has been presented with absence seizures. MRI demonstrated the hemispheric atrophy. Electroencephalography (EEG) demonstrated generalized 3 Hz spike and wave discharges. During follow up, the patient was seizure free with appropriate antiepileptic therapy

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1)Dyke CG, Davidoff LM, Masson CB. Cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Surg Gynecol Obstet. 1933; 57: 588-600.
2)Pendse NA, Bapna P, Menghani V, Diwan A. Dyke-Davidoff-Masson syndrome (DDMS). Indian J Pediatr. 2004; 71: 943.
3)Solomon GE, Hilal SK, Gold AP, Carter S. Natural history of acute hemiplegia of childhood. Brain. 1970; 93: 107-20.
4)Sener RN, Jinkins JR. MR of craniocerebral hemiatrophy. Clin İmaging. 1992; 16: 93-7.
5)Aguiar PH, Liu CW, Leitão H, et al. MR and CT imaging in the Dyke-Davidoff-Massonsyndrome. Report of three cases and contribution topathogenesis and differential diagnosis. Arq Neurosiquiatr. 1998; 56: 803-7.
6)Garg RK, Karak B. Cerebral hemiatrophy: a possible etiological relation with febrile seizures. Indian Pediatr. 1998; 35: 79-81.
7)Sharma S, Goyal D, Negi A, Sood RG, Jhobta A, Surya M. Dyke-Davidoff Mason Syndrome. Ind J Radiol Imag. 2006; 16: 165-6.
8)Shetty DS, Lakhkar NB, John JR. Dyke-Davidoff-Masson syndrome. Neurology India. 2003; 51: 136-9.
9)Ono K, Komai K, Ikeda T. Dyke-Davidoff-Mason syndrome manifested by seizure in late childhood: a case report. J Child Neurosci. 2003; 10: 367-71.