Yasemin BARANOĞLU KILINÇ, Ayşegül DANIŞ, Sıddıka HALICIOĞLU

Langerhans hücreli histiyositoz ile ilişkili bir çocukluk çağı sekonder baş ağrısı vakası

Langerhans hücreli histiyositoz (LHH) tanılı hastalarda nörolojik tutulum oldukça nadirdir. Hastalığın seyri sırasında sistemik etkilere ek olarak baş ağrısı da görülebilir. 6 yaşında kız hasta herhangi bir sistemik semptomu olmaksızın sadece baş ağrısı şikayeti ile hastaneye başvurdu ve LHH tanısı aldı. Manyetik rezonans görüntülemede, sfenoid kemik korpusundan sfenoid kemiğin sol büyük kanadına, sol orbital apekse, sol posterior etmoid hücrelere, sol kavernöz sinüse ve dural boşluğa uzanan katı bir kitle olduğu tespit edildi. Baş ağrısı olan hastalarda nörogörüntüleme için doğru karar verilmesi mortalite ve morbidite açısından çok önemlidir. LHH’ nin sekonder bir baş ağrısı nedeni olabileceğinin göz ardı edilmemesi için başka bir sistemik bulgusu olmayan sadece baş ağrısı ile başvuran ve LHH tanısı konulan olgumuzu sunmaktayız.

Anahtar Kelimeler:

Başağrısı, histopatoloji, langerhans hücreli histiyositoz, nörogörüntüleme, pediatric

A childhood secondary headache case associated with Langerhans cell histiocytosis

Neurological involvement is very rare in patients with a diagnosis of Langerhans Cell Histiocytosis (LCH). During the course of the disease, headache can also be seen in addition to systemic effects. A 6 years old girl was admitted to the hospital with only a headache without any systemic symptoms and was diagnosed with LCH. Magnetic resonance imaging showed a solid mass extending from the sphenoid bone corpus to the left great wing of the sphenoid, left orbital apex, left posterior ethmoid cells, left cavernous sinus, and dural space. The correct decision for neuroimaging in patients with headaches is very important in terms of mortality and morbidity. We wanted to share our patient’s case who was diagnosed with LCH by presenting only with headache without any other systemic finding, to remind that LCH may be a secondary cause of headache.

Keywords:

Headache, histopathology, langerhans cell histiocytosis, neuroimaging, pediatrics,

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