Hatice UYGUN, İbrahim BUCAK, Yunus COŞAR, Hilal AYDIN, Mehmet TURĞUT

Çocuklarda nadir görülen bir Guillan Barre sendromu alt türü: Akut aksonal motor nöropati

Guillan Barre Sendromu en sık görülen akut, immün aracılı demiyelinizan poliradikulonöropatidir. Guillan Barre Sendromu klinik ve elektrofizyolojik bulgularına göre alt türlere ayrılır. Bu alt türlerden birisi olan akut aksonal motor nöropati çocuklarda çok nadir görülür. Bu çalışmada ayaklarında ve ellerinde uyuşma, gözlerini tam olarak kapatamama, peltek konuşma, ıslık çalamama şikâyeti ile başvuran ve fizik muayenesinde hiperrefleksi saptanan akut aksonal motor nöropati tanılı on altı yaşındaki erkek olguyu sunuyoruz.

Anahtar Kelimeler:

Çocuk, Guillan Barre Sendromu, Nöropati

A rare subtype of Guillain Barre syndrome in children: Acute axonal motor neuropathy

Guillan Barre Syndrome is the most common acute, immune-mediated demyelinating polyradiculoneuropathy. Guillan Barre Syndrome is divided into subtypes based on clinical and electrophysiological findings. Acute axonal motor neuropathy, one of these subtypes, is very rare in children. In this study, we present a sixteen-year-old male patient with a diagnosis of acute axonal motor neuropathy, who presented with numbness in his feet and hands, inability to close his eyes fully, slurred speech, and inability to whistle, and hyperreflexia was found in his physical examination.

Keywords:

Child, Guillan Barre syndrome, Neuropathy,

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