Güray Toğral, Murat Arıkan, Fisun Ardıç Yükrük, Fatih Eksioğlu, Şafak Güngör

Nadir Görülen Femur Distal Yumuşak Doku Yerleşimli Parakordoma: Olgu Sunumu

Parakordoma myoepitelyoma olarak da isimlendirilen aksiyel dışı yerleşimli histolojik olarak kordomaya benzeyen yumuşak dokuların son derece nadir görülen bir tümörüdür. Bu nadir tümör extra-axial kordoma, parakordoma ya da kordoma periferikum olarak da adlandırılmaktadır. Lezyonlar daha sıklıkla erkeklerde görülür. Alt ekstremite en sık görülen lokalizasyon bölgesidir. Tedavisi öncelikle cerrahidir. İyi huylu bir tümör olmasına rağmen lokal agresif bir davranış gösterebilmektedir. Geç rekürrens gösterebilmekle birlikte nadirde olsa akciğer metastazı yapma potensiyelleri vardır. Bu olguda uyluk distalinden kaynaklanan ve çok nadir görülen bir parakordoma olgusu incelenmiştir.

Anahtar Kelimeler:

Parakordoma, femur distali, geniş rezeksiyon, histopatolojik bulgular

Rare Soft Tissue Localized Distal Femur Parachordoma: Case Presentation

Parachordoma, also named as myoepithelioma, is a rare,non axially located soft tissue tumor histologically resembling chordoma. This rare entity is also named as extra axial chordoma, parachordoma and chordoma periphericum. Lesions are generally seen in male patients and located at the lower extremities. The primary treatment modality is surgery. Even this tumor is benign, it may show local aggressive potential. Late local recurrences can be expected and pulmoner metastases are seldom. In this case presentation, a rare parachordoma case located at the distal femur is evaluated.

Keywords:

Parachordoma, distal femur, wide resection, histopathological findings,

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