Binhan Kağan Aktaş, Cüneyt Özden, Mehmet Murat Baykam, Remzi Salar, Mehmet Karabakan, Doğan Dede, Ali Memiş

Konjenital Pelvik Arteriovenöz Malformasyona Bağlı Spontan Masif Hematüri

Konjenital pelvik arteriyovenöz malformasyon nadir görülen bir hastalık olup genellikle asemptomatiktir. Pelvik arteriyovenöz malformasyonlar sıklıkla tümörlere, pelvik travmaya veya cerrahi işlemlere sekonder akkiz lezyonlardır. Bu makalede konjenital pelvik arteriyovenöz malformasyon nedeniyle spontan masif hematüri gelişen 72 yaşındaki bir bayan hastayı sunuyoruz. Başvuru anında hastanın hemoglobin ve hematokrit değerleri sırasıyla 7.2 g/dL ve %22'ye kadar düşmüştü. Öncelikle hastaya kan replasmanı yapıldı ve mesanedeki hematom boşaltılıp sistoskopik değerlendirmeye gidildi. Sistoskopide mesane tabanında yer yer eritemli alanlar ve pulsasyon şeklinde bir hareketlilik gözlendi. Bunun ardından çekilen bilgisayarlı tomografide pelvik kavitede vasküler malformasyonlar halinde lezyonlar tespit edilen hastanın kesin tanı ve tedavisi anjiografik olarak yapılmıştır. Anahtar kelimeler: Arteriovenöz Malformasyonlar; Hematüri; Mesane.

Anahtar Kelimeler:

Arteriovenöz Malformasyonlar; Hematüri; Mesane.

Spontaneous Massive Hematuria Due To Congenital Pelvic Arteriovenous Malformation

Congenital pelvic arteriovenous malformation is a rare disease that is usually asymptomatic. Pelvic arteriovenous malformations are often acquired lesions secondary to neoplasms, pelvic trauma or surgical procedures. In this paper, we present a case of spontaneous massive hematuria due to congenital pelvic arteriovenous malformation in a 72-year-old woman. At the time of admission, the patient's hemoglobin and hematocrit values had fallen to 7.2 g/dL and 22%, respectively. First, blood transfusion was done and cystoscopic evaluation was performed after hematoma in bladder was drained. At the cystoscopy, a pulsatile movement and erythematous areas were observed in the base of the bladder. Subsequently, vascular lesions in the pelvic cavity were detected by computed tomography and angiography was performed for definitive diagnosis and treatment of the patient. Key words: Arteriovenous Malformations; Hematuria; Urinary Bladder.

Keywords:

Arteriovenous Malformations; Hematuria; Urinary Bladder.,

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