Cogan Sendromlu Bir Olgu+

Cogan sendromu göz ve kulak tutulumunun birlikte görüldüğü inflamatuar damarsal bir hastalıktır. Gözde interstisyel keratit, kulakta odyovestibüler disfonksiyon bulguları ile karakterizedir. Cogan sendromlu hastalarda büyük ve orta büyüklükteki damarları tutan vaskülit izlenebilmektedir. Cogan Sendromunda erken tanı ve sistemik kortikosteroid tedavisi göz bulgularının ilerlememesi ve kalıcı sağırlık gelişimini önlemesi açısından çok önemlidir. Bu çalışmada geç tanı alan ve kalıcı sağırlık gelişen bir olgu irdelenmiştir. Anahtar kelimeler: Cogan sendromu, İnterstisyel keratit, Odyovestibuler disfonksiyon

Anahtar Kelimeler:

Cogan sendromu, İnterstisyel keratit, Odyovestibuler disfonksiyon

Case Report of Cogan Syndrome

Cogan syndrome is an inflammatory vascular disease with involvement of eye and ear. Cogan syndrome consists of interstitial keratitis associated with vestibuloauditory dysfunction. The disease has a predilection for large and medium sized blood vessels. Early diagnosis of Cogan syndrome is important because prompt treatment of the cochlear symptoms with systemic steroids may prevent permanent and profound deafness. A case of Cogan syndrome in chronic stage is represented in this report. Key words: Cogan syndrome, Interstitial keratitis, Audiovestibular dysfunction

Keywords:

Cogan syndrome, Interstitial keratitis, Audiovestibular dysfunction,

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