Bayram Ali DORUM, Hilal ÖZKAN, Nilgün KÖKSAL, Yasemin Denkboy ONGEN

Class I pentalogy of Cantrell: a rare case report

Pentalogy of Cantrell is characterized by the presence of five major congenital defects involving the abdominal wall, pericardium, diaphragm, lower sternum and various cardiac abnormalities. This rare syndrome was described by Cantrell in 1958 and it has poor prognosis. We report here a case of class I Cantrell syndrome and our aim is to share difficulties experienced and review the related literature.

Keywords:

Cantrell syndrome, ectopia cordis, omphalocele, ventricular diverticulum,

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