Prune belly syndrome associated with bilateral multicystic dysplastic kidneys and urethral obstruction: case report

Prune belly syndrome associated with bilateral multicystic dysplastic kidneys and urethral obstruction: case report

Prune belly syndrome is rare congenital disorder defined by characteristic clinical triad: Abdominal muscle deficiency. severe urinal}r tract abnormalities. and bilateral cryptorchidism. We describe preterm neonate of Prune Belly syndrome who had abdominal muscle deficiency. multicystic dysplastic kidney. urethral hypoplasia and pulmonary hypoplasia. We presented this rare case with the data gathered from the literatüre.

Kaynakça

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