Association of posterior urethral valve with congenital lobar emphysema: A case report

Posterior Urethral Valve (PUV) is the most common cause of bladder outlet obstruction in boys, with an incidence of 1 in 5,000 to 8,000 male births. Congenital lobar emphysema (CLE) is an uncommon cause of congenital pulmonary airway malformation, with an incidence 1 per 20,000 to 30,000 deliveries. These congenital malformations have never been described together before. A boy newborn with prenatal suspicion of PUV, confirmed in first days of live presented respiratory distress that lead CLE diagnosis. Our multidisciplinary team submitted him to a twostep surgery correction successfully.

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Malin G, Tonks AM, Morris RK, Gardosi J, Kilby MD. Congenital lower urinary tract obstruction: a population-based epidemiological study. BJOG. ;119(12):1455-64.

Correia-Pinto J, Gonzaga S, Huang Y, Rottier R. Congenital lung lesions-- underlying molecular mechanisms. Semin Pediatr Surg. 2010;19(3):171-9.

Heikkilä J, Taskinen S, Toppari J, Rintala R. Posterior urethral valves are often associated with cryptorchidism and inguinal hernias. J Urol. 2008; (2):715-7.

Rajab A, Freeman NV, Patton M. The frequency of posterior urethral valves in Oman. Br J Urol. 1996; 77(6):900-4.

Karnak I, Senocak ME, Ciftci AO, Buyukpamukçu N. Congenital lobar emphysema: diagnostic and therapeutic considerations. J Pediatr Surg. 1999; 34(9):1347-51.

Khemiri M, Khaldi F, Ben Becher S, Chaouachi B, Houissa T, Barsaoui S. Congenital lobar emphysema. Report of 17 cases. Tunis Med. 2008;86(4): 373-7.

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