Tolga ÖZDEMİRKIRAN, Ümit TAHTACI, Mehmet ÇELEBİSOY

Kavernöz hemanjioma bağlı orbital apex sendromu

Orbital apex sendromu; optik kanal bölgesinde inflamatuar, infeksiyöz, neoplastik, travmatik, vasküler ve bazen iatrojenik nedenlere bağlı olarak 2,3,4 ve 6. kranial sinirler ile 5. kranial sinirin oftalmik dalının tutulumu ile karakterizedir. Tedavi altta yatan nedene bağlı olup biyopsi yol gösterici olabilir. Hemanjiomlar orbitanın en sık primer tümöral oluşumlarından olmasına rağmen "Orbital Apex Sendromu"nun bir nedeni olarak kavernöz hemanjiom saptanması oldukça nadirdir. Orbital Manyetik Rezonans Görüntüleme (MRG) kitlenin tanınmasında ve ayırıcı tanıda oldukça yararlıdır.Erken tanı ve cerrahi tedavi ile morbidite azaltılabilir.

Orbital apex syndrome due to cavernous hemangioma

Orbital apex syndrome is characterized by the involvement of the 2,3,4 and 6th cranial nerves with the paralysis of ophtalmic branch of the 5th cranial nerve due to inflammatory, infectious, neoplastic, travmatic, vascular and sometimes iatrogenic reasons in the ophtalmic canal region. Biopsy from the resposible lesion can guide the tretment and it may be very informative.Altough the hemangiomas are the most common primary tumor of the orbit, cavernous hemangiomas as a cause of the "Orbital apex syndrome" is very uncommon. Orbital Magnetic Resonance Imaging (MRI) is a very useful tool to detect the mass lesion in the orbit and for the distinctive diagnosis. Morbidity can be decresed with the early diagnosis and early surgical teratment.

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