Cochlear implantation in a patient with Usher's syndrome

ISSN: 1019-1941
Yayın Aralığı: Yılda 3 Sayı
Başlangıç: 1988
Yayıncı: Marmara Üniversitesi

Usher's Syndrome is an autosomal recessive disorder characterized by congenital hearing loss and retinitis pigmentosa. Usher's Syndrome patients with severe to profound sensorineural hearing loss can be considered as candidates for cochlear implantation. This case study reports a deaf-blind with Usher's Syndrome who received a cochlear implant, the audiological evaluation is presented and the therapy sessions are discussed. The patient demonstrated good performance overtime after the implantation including open set speech understanding and telephone use.

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/. Qorlin RJ. Genetic hearing loss with eye disorders. In: Qorlin RJ, Tori ello HV, Cohen MM, eds. Hereditary Hearing Loss and Its Syndromes.Mew York: Oxford University Press, 1995:105-140.
2. Young NM, Johnson JC, Mets MB, Hain TC. Cochlear implants in young children with Usher's Syndrome. Ann Otol Rhinol Laryngol (Suppl), 1995 ;166:342-345. 3. Hinderink JB, Brokx JPL, Mens LH, Van Den Broek P. Results from four cochlear implant patients with Usher's Syndrome. Ann Otol Rhinol Laryngol 1994; 103:285-293. 4. Saeed SR, Ramsden RT, Axon PR. Cochlear implantation in the deaf-blind.Am J Otol 1998:19:774-777.