Nadir Görülen Bir Paraneoplastik Sendrom; Sweet Sendromu

Paraneoplastiksendrom; primer tümöre veya metastazlarına ait bir etki sebebi ile oluşmayan ancak tümörün varlığına bağımlı olarak gelişen belirti ve bulgulardan oluşan klinik tablo olarak adlandırılır. Paraneoplaziler varlığı bilinen bir tümörün seyri sırasında görülebildiği gibi, klinik olarak ortaya çıkmamış gizli bir tümörün ilk ve tek belirtisi olabilir ve bu sayede primer kanserin erken evrede tanınmasına yardımcı olabilmektedir. Akut febrilnötrofilik dermatoz olarak da bilinen Sweet Sendromu; ani başlangıçlı, ağrılı, inflamatuvar papül veya nodüllerden oluşmuş eritemli plaklar, ateş, eklem ağrısı, periferiklökositoz ve cildin dermis tabakasında yoğun nötrofil infiltrasyonu ile karakterize nadir görülen tekrarlayan inflamatuvar bir cilt hastalığıdır. Hastalık; inflamatuar bağırsak hastalığı, enfeksiyonlar, ilaçlara sekonder, malignite yesekonder (paraneoplastik) olarak gözlemlenebilmektedir.Bu yazımızda akut gelişen döküntü ve ateş şikayetleri ile başvurduğu hastanede Sweet Sendromu ön tanısı ile interne edilen yapılan etyolojik araştırmasında metastatik akciğer karsinoid tümör tanısı konulan 69 yaşında erkek hasta ile ilgili bir olgu sunmayı amaçladık.

Anahtar Kelimeler:

Sweet Sendromu, Paraneoplastik Sendrom, Akciğer Kanseri

A Rare Paraneoplastic Syndrome; Sweet Syndrome

Paraneoplastic syndrome; It is called a clinical Picture that does not ocur due to an effect of the primary tumor or its metastases, but consists of signs and symptoms that develop depending on the presence of the tumor. Paraneoplasias can be seenduring the course of a tumorwith a known presence, and may be the first and onlysymptom of a hiddentumorthat has not emergedclinically, thushelping to identifyprimarycancer at an earlystage. Sweet'sSyndrome, alsoknown as acutefebrileneutrophilicdermatosis; It is a rare, recurrentinflammatory skin diseasecharacterizedbysuddenonset, painful, inflammatorypapulesornoduleswitherythematousplaques, fever, jointpain, peripheralleukocytosis and intenseneutrophilinfiltration in the dermislayer of the skin. Disease; It can be observed as inflammatoryboweldisease, infections, secondary to drugs, secondary to malignancy (paraneoplastic). In this article, weaimed to present a case of a 69-year-old malepatientwhowasdiagnosedwithmetastaticlungcarcinoidtumor in the etiologicalinvestigationperformedwith the pre-diagnosis of SweetSyndrome in the hospitalwhere he presentedwithcomplaints of acuterash and fever.

Keywords:

Sweet Syndrome, Paraneoplastic Syndrome, Lung Cancer,

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