Zinner’s Syndrome: Case Report of a Rare Maldevelopment in the Male Genitourinary Tract

Zinner’s syndrome is a rare embryologic anomaly of the distal portion of the mesonephric duct comprising a triad of ipsilateral renal agenesis, seminal vesicle cyst and ejaculatory duct obstruction. We report ultrasound and magnetic resonance imaging findings of this rare developmental anomaly involving the mesonephric duct, in an asymptomatic 17-year-old boy who would probably remain undiagnosed until later age. The patient presented with no specific symptoms and was incidentally diagnosed on imaging exams.

Zinner Sendromu: Erkek Ürogenital Sistemde Nadir Görülen Bir Gelişim Bozukluğu Olgusu

Zinner sendromu; ipsilateral renal agenezi, seminal vezikül kisti ve ejakülatör kanal obstrüksiyon triadını içeren, mezonefrik kanalın distal kısmında nadir görülen, embriyolojik bir anomalidir. Muhtemelen daha sonraki yaşlara kadar tanı konulmadan kalacak olan 17 yaşındaki asemptomatik bir erkek çocukta, mezonefrik kanalı tutan bu nadir gelişimsel anomalinin ultrason ve manyetik rezonans görüntüleme bulgularını sunuyoruz. Spesifik bir semptomu bulunmayan hastaya, görüntülenme muayenelerinde tesadüfen tanı konulmuştur.

Kaynakça

1. Pereira BJ, Sousa L, Azinhais P, Conceição P, Borges R, Leão R, Brandão A, Temido P, Retroz E, Sobral F. Zinner’s syndrome: an up-to-date review of the literature based on a clinical case. Andrologia 2009;41:322-330.

2. Livingston L, Larsen CR. Seminal vesicle cyst with ipsilateral renal agenesis. AJR Am J Roentgenol 2000;175:177-180.

3. King BF, Hattery RR, Lieber MM, Berquist TH, Williamson Jr B, Hartman GW. Congenital cystic disease of the seminal vesicle. Radiology 1991;178:207- 211.

4. Fiaschetti V, Greco L, Giuricin V, De Vivo D, Di Caprera E, Di Trapano R, Castellani F, Floris R. Zinner syndrome diagnosed by magnetic resonance imaging and computed tomography: role of imaging to identify and evaluate the uncommon variation in development of the male genital tract. Radiol Case Rep 2017;12:54-58.

5. Mehra S, Ranjan R, Chandra Garga U. Zinner syndrome - a rare developmental anomaly of the mesonephric duct diagnosed on magnetic resonance imaging. Radiol Case Rep 2016;11:313-317.

6. Slaoui A, Regragui S, Lasri A, Karmouni T, El Khader K, Koutani A, Ibn Attya A. Zinner’s syndrome: report of two cases and review of the literature. Basic Clin Androl 2016;26:10.

7. Rappe BJM, Meuleman EJH, Debruyne FMJ. Seminal vesicle cyst with ipsilateral renal agenesis. Urol Int 1993;50:54-56.

8. Sundar R, Sundar G. Zinner syndrome: an uncommon cause of painful ejaculation. BMJ Case Rep 2015:2015.

9. Kiremit MC, Acar O, Sag AA, Koseoglu E, Kilic M, Kordan Y, Balbay MD. Minimally invasive management of Zinner’s syndrome with same-session robot-assisted seminal vesiculectomy and ipsilateral nephroureterectomy using a single geometry of trocars. J Endourol Case Rep 2018;4:186-189.

Kaynak Göster

  • ISSN: 2148-9580
  • Yayın Aralığı: Yılda 4 Sayı
  • Başlangıç: 2014

2.5b 1.7b

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