Fadwa ALLOUCHE, Asmae MAZTİ, Fatima Zahra TERRAB, Sanae GHAMMAD, Touria BOUHAFA, Abderrahmane EL MAZGHİ, Khalid HASSOUNİ

Böbrek berrak hücreli sarkom: Bir olgu hakkında

Böbrek Berrak Hücreli Sarkom (SRCC), saldırganlığı, yüksek kemik metastatik potansiyeli ve tekrarlama eğilimi nedeniyle tanınan, çocuğun nadir görülen malign tümörüdür. Büyük bir sağ lomber kitle olan 22 aylık bir bebekte SRCC tanısı alan bir olgu sunuyoruz. Bu kitlenin tanısı bir anatomi-patoloji üzerine yerleştirilmiş şeffaf hücreli sarkomu olup, böbrek kitlesinin tanısı böbrek kanseri ile ilgili belirsiz kalmıştır. Histolojik özellik dışında, şu anda tanısı için bir kriter bulunmamaktadır. Yeni tedavi rejimlerinin uygulamaya konması ile prognozu belirgin bir şekilde artmıştır.

Anahtar Kelimeler:

Tümör, Böbrek, Çocuk, Sarkoma, Berrak hücreler

Kidney clear cell sarcoma: About one case

Kidney Clear Cell Sarcoma (SRCC) is a rare malignant tumor of the child, recognized for its aggressiveness, its high bone metastatic potential and its tendency to recur. We report a case diagnosed SRCC in a 22-month-old infant with a large right lumbar mass. An observation of Kidney tumor type clear-cell sarcoma, whose diagnosis was placed on a piece of anatomo-pathology, insofar as the imaging remained uncertain as to the Kidney origin of this mass. Apart from the histological aspect, there is currently no criterion for its diagnosis. Its prognosis has been markedly improved by the introduction of new treatment regimens.

Keywords:

Tumor, Kidney, Child, Sarcoma, Clear cells,

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