Merve AKSUNGUR, Dilek DİLLİ, İrfan TAŞOĞLU, Başak SORAN TÜRKCAN, Utku Arman ÖRÜN, Rumeysa ÇİTLİ, Hasan AKDUMAN, Gülşen AVCIOĞLU, Gizem GÜNEŞ

Kesintili aortik ark: Yasui ameliyatı sonrası yenidoğan yoğun bakım ünitesi yönetimi

Kesintili aortik ark (KAA) neonatal dönemde bulgu veren oldukça karmaşık ve yönetimi zor bir konjenital kalp hastalığıdır (KKH). Bu vakalarda, çıkan ve inen aorta arasında anatomik ve luminal kesinti vardır. KAA, geçmişte mortalitesi yüksek olan ancak günümüzde yaşam beklentisi giderek artan bir kardiyak anomalidir. KAA’nın tedavisi cerrahi olarak arkus tamiri yapılmasıdır. Sol ventrikül çıkım yolu (LVOT) darlığının eşlik etmesi daha komplike cerrahi teknikleri uygulanmasını gerektirir. Bu yazıda tip B KAA ve LVOT darlığı nedeniyle Yasui prosedürü uygulanan ve postoperatif 12. günden sonra yenidoğan yoğun bakım ünitesinde izlenen bir bebeğin yoğun bakım sürecinden yola çıkarak kardiyak hasta izlem ilkeleri tartışılmaktadır. Açık kalp cerrahisi yapılan bebek hastaların yönetimi konusundaki deneyimlerin kardiyak bakım ile ilgilenen yenidoğan hemşire ve doktor ekipleri için yararlı olması amaçlanmıştır.

Anahtar Kelimeler:

Kesintili aortik ark, sol ventrikül çıkım yolu darlığı, Yasui ameliyatı, yenidoğan yoğun bakım, yönetim

Intensive care follow-up of an infant who underwent Yasui procedure due to interrupted aortic arch and left ventricular outflow tract obstruction

Interrupted aortic arch (IAA) is a highly complex and difficult to manage congenital heart disease (CHD) manifesting in the neonatal period. In these cases, there is an anatomical and luminal interruption between the ascending and descending aorta. Formerly, IAA was considered to be a cardiac anomaly with high mortality, but nowadays its life expectancy is getting higher. The treatment of IAA is surgical repair of the arch. The presence of left ventricular outflow tract obstruction (LVOTO) requires more complicated surgical techniques. In this article, the intensive care process of a baby who underwent Yasui procedure for type B IAA and LVOTO and followed-up in neonatal intensive care unit after postoperative day 12 was discussed within the framework of cardiac patient monitoring principles.We aim that our experiences on the management of infant patients undergoing open heart surgery will be beneficial for nurses and physicians dealing with heart care.

Keywords:

Interrupted aortic arch, left ventricular outflow tract obstruction, Yasui surgery, neonatal intensive care, management,

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